Carnitine palmitoyltransferase I (CPT1) also known as carnitine acyltransferase I, CPTI, CAT1, CoA:carnitine acyl transferase (CCAT), or palmitoylCoA transferase...
19 KB (2,459 words) - 01:45, 1 May 2024
Carnitine palmitoyltransferase I deficiency is a rare metabolic disorder that prevents the body from converting certain fats called long-chain fatty acids(LCFA)...
7 KB (597 words) - 14:52, 27 October 2023
Carnitine palmitoyltransferase II deficiency, sometimes shortened to CPT-II or CPT2, is an autosomal recessively inherited genetic metabolic disorder characterized...
26 KB (3,167 words) - 04:46, 1 May 2024
Carnitine O-palmitoyltransferase 2, mitochondrial is an enzyme that in humans is encoded by the CPT2 gene. Carnitine palmitoyltransferase II precursor...
9 KB (1,034 words) - 23:07, 18 January 2024
Carnitine O-palmitoyltransferase (also called carnitine palmitoyltransferase) is a mitochondrial transferase enzyme (EC 2.3.1.21) involved in the metabolism...
2 KB (151 words) - 07:15, 20 October 2022
acetylcarnitine ester and being transported by carnitine palmitoyltransferase I and carnitine palmitoyltransferase II. Carnitine also plays a role in stabilizing acetyl-CoA...
30 KB (3,278 words) - 20:35, 26 April 2024
"Structural model of a malonyl-CoA-binding site of carnitine octanoyltransferase and carnitine palmitoyltransferase I: mutational analysis of a malonyl-CoA affinity...
4 KB (493 words) - 14:06, 13 October 2022
Carnitine palmitoyltransferase I deficiency (CPT) - Carnitine palmitoyltransferase I Carnitine palmitoyltransferase II deficiency (CPT) - Carnitine palmitoyltransferase...
4 KB (356 words) - 21:16, 7 December 2020
dextrorotatory (R)-(+)- enantiomer, is an irreversible inhibitor of carnitine palmitoyltransferase-1 (CPT-1; EC 2.3.1.21) on the inner face of the outer mitochondrial...
17 KB (1,783 words) - 07:25, 22 April 2024
(downstream of glycolysis) and an allosteric inhibitor of Carnitine palmitoyltransferase I (CPT1), a mitochondrial enzyme important for bringing fatty...
24 KB (2,820 words) - 02:59, 22 November 2023