• Acyl-CoA dehydrogenases (ACADs) are a class of enzymes that function to catalyze the initial step in each cycle of fatty acid β-oxidation in the mitochondria...
    17 KB (2,171 words) - 04:03, 25 March 2024
  • Thumbnail for Medium-chain acyl-coenzyme A dehydrogenase deficiency
    Medium-chain acyl-CoA dehydrogenase deficiency (MCAD deficiency or MCADD) is a disorder of fatty acid oxidation that impairs the body's ability to break...
    15 KB (1,670 words) - 22:40, 29 December 2023
  • Thumbnail for Acyl-CoA
    Acyl-CoA is a group of coenzymes that metabolize fatty acids. Acyl-CoA's are susceptible to beta oxidation, forming, ultimately, acetyl-CoA. The acetyl-CoA...
    10 KB (1,190 words) - 10:15, 10 April 2024
  • by acyl CoA dehydrogenase to produce trans-delta 2-enoyl CoA. It uses FAD as an electron acceptor and it is reduced to FADH2. Trans-delta 2-enoyl CoA is...
    32 KB (3,362 words) - 03:59, 23 May 2024
  • Thumbnail for Very long-chain acyl-coenzyme A dehydrogenase deficiency
    long-chain-acyl-dehydrogenase) deficiency is exclusively linked to genetic mutations in DNA. A change of the gene that codes for very long-chain-acyl-CoA-dehydrogenase...
    10 KB (1,061 words) - 09:28, 26 July 2023
  • Thumbnail for Short-chain acyl-coenzyme A dehydrogenase deficiency
    developmental delays, and microcephaly. The symptoms of short-chain acyl-CoA dehydrogenase deficiency may be triggered during illnesses such as viral infections...
    9 KB (709 words) - 22:51, 29 April 2024
  • Thumbnail for ACADS
    Acyl-CoA dehydrogenase, C-2 to C-3 short chain is an enzyme that in humans is encoded by the ACADS gene. This gene encodes a tetrameric mitochondrial flavoprotein...
    10 KB (1,232 words) - 23:12, 6 February 2024
  • ISSN 1879-0038. PMC 7949704. PMID 33450351. "#231680 - MULTIPLE ACYL-CoA DEHYDROGENASE DEFICIENCY; MADD". www.omim.org. Retrieved 2023-12-06. "Glutaric...
    9 KB (941 words) - 20:31, 14 December 2023
  • Thumbnail for Long-chain 3-hydroxyacyl-coenzyme A dehydrogenase deficiency
    inadequate levels of an enzyme called long-chain 3-hydroxyacyl-coenzyme A (CoA) dehydrogenase, which is part of a protein complex known as mitochondrial trifunctional...
    4 KB (331 words) - 00:31, 25 April 2022
  • Thumbnail for Short-chain acyl-CoA dehydrogenase
    Short-chain acyl-CoA dehydrogenase (EC 1.3.8.1, butyryl-CoA dehydrogenase, butanoyl-CoA dehydrogenase, butyryl dehydrogenase, unsaturated acyl-CoA reductase...
    4 KB (431 words) - 03:14, 30 March 2024